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DNA-testable inherited disorders in companion animals — OMIA characterised causal variants by species, gene and pathogenicity class

dna_test_matrix_companion_inherited_disorders

dna-test-matrix 6192 tok en 2026-08-24

DNA-testable inherited disorders in companion animals — OMIA characterised causal variants by species, gene and pathogenicity class

Derived from the OMIA database dump (omia.xml; Nicholas, F.W., Tammen, I., & Sydney Informatics Hub. (2026). Online Mendelian Inheritance in Animals (OMIA) [dataset]. https://omia.org/. https://doi.org/10.25910/2AMR-PV70). This compilation lists every companion-animal phene for which OMIA records a characterised causal variant — the set of inherited disorders that are in principle DNA-testable. Structured fields (gene, chromosome, cDNA/protein change, rsID, pathogenicity class) are first-hand values from the OMIA Variant and PathogenicityClassification tables, traceable line-by-line to pdf-raw/omia/dna_test_matrix_companion.txt; pathogenicity classes follow ACMG-style labels (P = pathogenic, LP = likely pathogenic, VUS = variant of uncertain significance, LB/B = likely benign/benign). Livestock and laboratory-model species are excluded by design. Data made available by software support from the Sydney Informatics Hub, funded from the Ronald Bruce Anstee bequest to the Sydney School of Veterinary Science for the Anstee Hub for Inherited Diseases in Animals (AHIDA). FAIR use with attribution confirmed by OMIA curator (A/Prof I. Tammen) 2026-08-22.

122 disorders, 122 characterised variants, 6 companion species/taxa. Each disorder links back to its OMIA entry.

Dog (Canis lupus familiaris)

DisorderGenecDNA changeProtein changersIDClassOMIA
Adrenal cortical atrophyXM_012178620.3:c.645_648delXP_012034010.1:p.(L215Ffs*34)Not currently evaluated[OMIA16](https://omia.org/OMIA000016/9615/)
Afibrinogenaemia or hypofibrinogenaemiaNot currently evaluated[OMIA18](https://omia.org/OMIA000018/9615/)
Alopecia, genericNM_001048133.1:c.-24_32delP[OMIA30](https://omia.org/OMIA000030/9615/)
AphakiaNM_001314111.1:c.656C>TNP_001301040.1:p.(P219L)Not currently evaluated[OMIA54](https://omia.org/OMIA000054/9615/)
Autoimmune thrombocytopeniaMafa_ABOp.266L + p.268GNot currently evaluated[OMIA95](https://omia.org/OMIA000095/9615/)
Axonopathy, progressiveNot currently evaluated[OMIA825](https://omia.org/OMIA000825/9615/)
Blood group systems, genericNot currently evaluated[OMIA116](https://omia.org/OMIA000116/9615/)
Calcinosis circumscriptaXM_042246797.1:c.2908G > AXP_042102731.1:p.(G970S)Not currently evaluated[OMIA158](https://omia.org/OMIA000158/9615/)
CardiomyopathyPrPp.(H143R)Not currently evaluated[OMIA160](https://omia.org/OMIA000160/9615/)
Cardiomyopathy, dilatedXM_038549826.1:c.261C>AXP_038405754.1:p.(Y87*)Not currently evaluated[OMIA162](https://omia.org/OMIA000162/9615/)
Chondrodysplasia, genericc.[124G>A;125_130del6]Not currently evaluated[OMIA187](https://omia.org/OMIA000187/9615/)
Conotruncal heart malformationsSCFRNot currently evaluated[OMIA224](https://omia.org/OMIA000224/9615/)
Coxofemoral dysplasiaNot currently evaluated[OMIA233](https://omia.org/OMIA000233/9615/)
Coxofemoral luxationc.819_820ins90Not currently evaluated[OMIA234](https://omia.org/OMIA000234/9615/)
Cushing syndrome, ACTH-dependent, pituitary-dependent hyperadrenocorticismNM_001197029.1:c.451C>TNP_001183958.1:p.(R151W)rs23373415Not currently evaluated[OMIA247](https://omia.org/OMIA000247/9615/)
Dermatomyositisp.(V311_K333del)Not currently evaluated[OMIA270](https://omia.org/OMIA000270/9615/)
Diamond-Blackfan anaemia, genericPLPT>ANot currently evaluated[OMIA41](https://omia.org/OMIA000041/9615/)
DysautonomiaGDF-8c.*1232G>ANot currently evaluated[OMIA312](https://omia.org/OMIA000312/9615/)
EntropionNM_001034039.2:c.4234G>ANP_001029211.1:p.(D1412N)Not currently evaluated[OMIA337](https://omia.org/OMIA000337/9615/)
Fucosidosis, alphaMC1-RNM_001008690.1:c.727G>ANP_001008690.1:p.(A243T)Not currently evaluated[OMIA396](https://omia.org/OMIA000396/9615/)
Gangliosidosis, GM1T1R2Not currently evaluated[OMIA402](https://omia.org/OMIA000402/9615/)
Gangliosidosis, GM2, genericXM_022425933.1:c.1643T>CXP_022281641.1:p.(V548A)Not currently evaluated[OMIA403](https://omia.org/OMIA000403/9615/)
Gaucher disease, genericNot currently evaluated[OMIA405](https://omia.org/OMIA000405/9615/)
Gingival hypertrophyNot currently evaluated[OMIA409](https://omia.org/OMIA000409/9615/)
GlomerulonephritisGDF8NM_001001525.3:c.871G>TNP_001001525.1:p.(E291*)rs5334475075Not currently evaluated[OMIA413](https://omia.org/OMIA000413/9615/)
Glomerulonephropathyp.(V311_K333del)Not currently evaluated[OMIA414](https://omia.org/OMIA000414/9615/)
Glossopharyngeal defectNot currently evaluated[OMIA415](https://omia.org/OMIA000415/9615/)
Glycogen storage disease VIIATP-PFKNot currently evaluated[OMIA421](https://omia.org/OMIA000421/9615/)
Goitre, familialTYRONot currently evaluated[OMIA424](https://omia.org/OMIA000424/9615/)
Haemolytic anaemia, primary autoimmuneNot currently evaluated[OMIA434](https://omia.org/OMIA000434/9615/)
Haemophilia Ac.574-589delNot currently evaluated[OMIA437](https://omia.org/OMIA000437/9615/)
Haemophilia BXM_006929856.5:c.1000G>AXP_006929918.1:p.(A334T)rs5334475117Not currently evaluated[OMIA438](https://omia.org/OMIA000438/9615/)
Heart defect, congenitalc.286C>Tp.(R96C)Not currently evaluated[OMIA446](https://omia.org/OMIA000446/9615/)
Hepatitis, neonatalNM_001244985.1:c.1603G>ANP_001231914.1:p.(D535N)rs5334475141Not currently evaluated[OMIA1094](https://omia.org/OMIA001094/9615/)
Hernia, hiatalNP_001098835.1:904G>ANP_001098835.1:p.(G302S)Not currently evaluated[OMIA461](https://omia.org/OMIA000461/9615/)
HyperkinesisGDF8NM_001001525.3:c.871G>TNP_001001525.1:p.(E291*)rs5334475075Not currently evaluated[OMIA503](https://omia.org/OMIA000503/9615/)
HyperlipoproteinaemiaPrPc.426A>Gp.(I142M)rs268292980Not currently evaluated[OMIA1210](https://omia.org/OMIA001210/9615/)
Hypotrichosis, genericc.1646delNot currently evaluated[OMIA540](https://omia.org/OMIA000540/9615/)
Immunodeficiencynullc.D153delNot currently evaluated[OMIA550](https://omia.org/OMIA000550/9615/)
Intestinal cobalamin malabsorption, AMN-relatedNot currently evaluated[OMIA565](https://omia.org/OMIA000565/9615/)
Masticatory muscle myositisXM_022419456.1:c.871C>TXP_022275164.1:p.(R291*)Not currently evaluated[OMIA1134](https://omia.org/OMIA001134/9615/)
MicrophthalmiaNot currently evaluated[OMIA649](https://omia.org/OMIA000649/9615/)
Mucopolysaccharidosis VIIc.574-589delNot currently evaluated[OMIA667](https://omia.org/OMIA000667/9615/)
MyastheniaNM_001048133.1:c.-24_32delP[OMIA684](https://omia.org/OMIA000684/9615/)
Myoclonus epilepsy of LaforaZFHX1BNot currently evaluated[OMIA690](https://omia.org/OMIA000690/9615/)
Nephritis, X-linkedSLC6A5c.809T>Cp.(L270P)rs3423560860Not currently evaluated[OMIA1112](https://omia.org/OMIA001112/9615/)
Neutropenia, cyclicNot currently evaluated[OMIA248](https://omia.org/OMIA000248/9615/)
Osmotic resistance of erythrocytesNot currently evaluated[OMIA746](https://omia.org/OMIA000746/9615/)
Patent ductus arteriosusPLPT>ANot currently evaluated[OMIA779](https://omia.org/OMIA000779/9615/)
Persistence of immature pyruvate kinase and hexokinase isozymesPLPT>ANot currently evaluated[OMIA790](https://omia.org/OMIA000790/9615/)
Persistent Mullerian duct syndrome, genericPLPT>ANot currently evaluated[OMIA791](https://omia.org/OMIA000791/9615/)
Prekallikrein deficiencyZFHX1BNot currently evaluated[OMIA819](https://omia.org/OMIA000819/9615/)
Renal dysplasiac.647-36_647-35insN[226]Not currently evaluated[OMIA1135](https://omia.org/OMIA001135/9615/)
Retinal atrophy - Rod-cone dysplasia 1PDBSNot currently evaluated[OMIA882](https://omia.org/OMIA000882/9615/)
Retinal atrophy - Rod-cone dysplasia, CRX relatedNot currently evaluated[OMIA881](https://omia.org/OMIA000881/9615/)
Sex reversal, generic (redundant)c.6119C>Tp.(T2020M)Not currently evaluated[OMIA900](https://omia.org/OMIA000900/9615/)
Shoulder luxationc.653_654insCp.(M114Hfs*16)Not currently evaluated[OMIA912](https://omia.org/OMIA000912/9615/)
Sodium-potassium-ATPase, high activityNot currently evaluated[OMIA924](https://omia.org/OMIA000924/9615/)
Sudden deathZFHX1BNot currently evaluated[OMIA955](https://omia.org/OMIA000955/9615/)
Tail, shortC20H19orf28XM_038567816.1:c.151C>TXP_038423744.1:p.(R51C)rs22915955Not currently evaluated[OMIA975](https://omia.org/OMIA000975/9615/)
TaillessnessNot currently evaluated[OMIA977](https://omia.org/OMIA000977/9615/)

Cat (Felis catus)

DisorderGenecDNA changeProtein changersIDClassOMIA
Achalasia of the oesophagus, congenitalrs654545998Not currently evaluated[OMIA3](https://omia.org/OMIA000003/9685/)
AnodontiaXM_014109833.2:c.107G>CXP_013965308.1:p.(C36S)rs1152388503Not currently evaluated[OMIA48](https://omia.org/OMIA000048/9685/)
Aorticopulmonary septal defectc.20-21dupNot currently evaluated[OMIA53](https://omia.org/OMIA000053/9685/)
Ataxia, genericXM_005637485.3:c.85G>AXP_005637542.1:p.(V29M)Not currently evaluated[OMIA77](https://omia.org/OMIA000077/9685/)
Atresia anic.33+1G>ANot currently evaluated[OMIA83](https://omia.org/OMIA000083/9685/)
Autoimmune thrombocytopeniaMafa_ABOp.266L + p.268GNot currently evaluated[OMIA95](https://omia.org/OMIA000095/9685/)
Axonopathy, peripheralXM_005624636.3:c.224G>AXP_005624693.1:p.(W75*)Not currently evaluated[OMIA99](https://omia.org/OMIA000099/9685/)
Blood group system ABTVANM_001044645.1:c.186C>GNP_001038110.1:p.(C62W)Not currently evaluated[OMIA119](https://omia.org/OMIA000119/9685/)
Cerebellar hypoplasiaNM_001048129.1:c.368-11T>Ars397511324Not currently evaluated[OMIA179](https://omia.org/OMIA000179/9685/)
Coat colour, pink-eyed dilutionNP_001098835.1:904G>ANP_001098835.1:p.(G302S)Not currently evaluated[OMIA212](https://omia.org/OMIA000212/9685/)
CyclopiaNot currently evaluated[OMIA249](https://omia.org/OMIA000249/9685/)
Dandy-Walker syndromeNot currently evaluated[OMIA258](https://omia.org/OMIA000258/9685/)
Diabetes mellitusNM_001009333.2:c.40delNP_001009333.2:p.(L14Sfs*82)P[OMIA279](https://omia.org/OMIA000279/9685/)
Diabetes mellitus, type 235DAGNot currently evaluated[OMIA284](https://omia.org/OMIA000284/9685/)
Ears, folded (drop vs prick)NM_173913.2:c.1057_1058delNP_776338.1:p.(Y353L)Not currently evaluated[OMIA319](https://omia.org/OMIA000319/9685/)
EctrodactylyZFHX1BNot currently evaluated[OMIA324](https://omia.org/OMIA000324/9685/)
EncephalomyelopathyNot currently evaluated[OMIA335](https://omia.org/OMIA000335/9685/)
Eye colourNot currently evaluated[OMIA357](https://omia.org/OMIA000357/9685/)
Eyelid gland, third, prolapse ofZFHX1BNot currently evaluated[OMIA359](https://omia.org/OMIA000359/9685/)
Fibrodysplasia ossificansNot currently evaluated[OMIA388](https://omia.org/OMIA000388/9685/)
Fucosidosis, alphap.(L530P)Not currently evaluated[OMIA396](https://omia.org/OMIA000396/9685/)
Gangliosidosis, GM2, genericXM_022425933.1:c.1643T>CXP_022281641.1:p.(V548A)Not currently evaluated[OMIA403](https://omia.org/OMIA000403/9685/)
Goitre, familialXM_022425933.1:c.1643T>CXP_022281641.1:p.(V548A)Not currently evaluated[OMIA424](https://omia.org/OMIA000424/9685/)
Haemophilia BNM_001192797.1:c.1222C>TNP_001179726.1:p.(H408T)rs5334475098Not currently evaluated[OMIA438](https://omia.org/OMIA000438/9685/)
Heart defect, congenitalED1Not currently evaluated[OMIA446](https://omia.org/OMIA000446/9685/)
HypoparathyroidismXM_038583131.1:c.673T>CXP_038439059.1:p.Y225HNot currently evaluated[OMIA528](https://omia.org/OMIA000528/9685/)
Hypotrichosis with thymic aplasia, congenitalc.1322G>Ap.(R441Q)Not currently evaluated[OMIA544](https://omia.org/OMIA000544/9685/)
Hypotrichosis, genericc.731G>Tp.(C244F)Not currently evaluated[OMIA540](https://omia.org/OMIA000540/9685/)
Megaoesophagus, genericXM_045050794.1:c.1180C>TXP_044906729.1:p.(R394*)rs7111000092Not currently evaluated[OMIA631](https://omia.org/OMIA000631/9685/)
MonorchidismXM_023617086.1:c.50G>AXP_023472854.1:p.(R17K)rs3447120064Not currently evaluated[OMIA659](https://omia.org/OMIA000659/9685/)
Muscular dystrophy, Duchenne typeNot currently evaluated[OMIA1081](https://omia.org/OMIA001081/9685/)
Olivopontocerebellar atrophyTYRONot currently evaluated[OMIA740](https://omia.org/OMIA000740/9685/)
Persistent Mullerian duct syndrome, genericPLPT>ANot currently evaluated[OMIA791](https://omia.org/OMIA000791/9685/)
Rectovaginal fistula (redundant)NM_001010944.1:c.124+1G>ANot currently evaluated[OMIA851](https://omia.org/OMIA000851/9685/)
Retinitis pigmentosa, peripherin-relatedNM_001009333.2:c.40delNP_001009333.2:p.(L14Sfs*82)P[OMIA871](https://omia.org/OMIA000871/9685/)
Sex reversal, generic (redundant)NM_001048133.1:c.-24_32delP[OMIA900](https://omia.org/OMIA000900/9685/)
Situs inversusNot currently evaluated[OMIA1102](https://omia.org/OMIA001102/9685/)
Waardenburg syndrome, genericNM_001197095.1:c.101dupNP_001184024.1:p.(A35Gfs*56)Not currently evaluated[OMIA1059](https://omia.org/OMIA001059/9685/)

Rabbit (Oryctolagus cuniculus)

DisorderGenecDNA changeProtein changersIDClassOMIA
Chondrodystrophyc.901+1G>ANot currently evaluated[OMIA189](https://omia.org/OMIA000189/9986/)
Coat colour, dominant whitec.1467C>Tp.(R512*)Not currently evaluated[OMIA209](https://omia.org/OMIA000209/9986/)
Ehlers-Danlos syndrome, genericNot currently evaluated[OMIA327](https://omia.org/OMIA000327/9986/)
Left ostium straightc.1400G>Tp.(G467V)Not currently evaluated[OMIA583](https://omia.org/OMIA000583/9986/)

Horse (Equus caballus)

DisorderGenecDNA changeProtein changersIDClassOMIA
Arytenoid chondritisNM_001103215.1:c.4726C>TNP_001096685.1:p.(R1576*)Not currently evaluated[OMIA74](https://omia.org/OMIA000074/9796/)
Atlanto occipital fusionXM_045038859.1:c.1017G>AXP_044894794.1:p.(W339*)Not currently evaluated[OMIA81](https://omia.org/OMIA000081/9796/)
Blood group systems, genericNM_001003343.1:c.2668C>TNP_001003343.1:p.(R890*)Not currently evaluated[OMIA116](https://omia.org/OMIA000116/9796/)
Coat colour, genericXM_011285657.3:c.160delXP_011283959.1:p.(H54Tfs*108)Not currently evaluated[OMIA200](https://omia.org/OMIA000200/9796/)
CribbingNM_001003009.2:c.1777C>TNP_001003009.2:p.(R593W)Not currently evaluated[OMIA241](https://omia.org/OMIA000241/9796/)
Dermal allergyNM_001003148.1:c.8392delNP_001003148.1:p.(Q2798Rfs*3)Not currently evaluated[OMIA268](https://omia.org/OMIA000268/9796/)
Difference of sexual development, genericMATPXM_001498110.4:c.449G>AXP_001498160.2:p.(R150Q)rs5334475197Not currently evaluated[OMIA564](https://omia.org/OMIA000564/9796/)
Exercise-induced pulmonary haemorrhageVMD2NM_001097545.1:c.482G>ANP_001091014.1:p.(G161D)Not currently evaluated[OMIA1896](https://omia.org/OMIA001896/9796/)
Haemophilia ANM_001048133.1:c.910G>ANP_001041598.1:p.(G304R)LP/P[OMIA437](https://omia.org/OMIA000437/9796/)
Hernia, umbilicalPLPT>ANot currently evaluated[OMIA465](https://omia.org/OMIA000465/9796/)
Hoof, flatc.984delp.(I330Sfs*2)Not currently evaluated[OMIA480](https://omia.org/OMIA000480/9796/)
Laryngeal paralysis, genericNP_001098835.1:904G>ANP_001098835.1:p.(G302S)Not currently evaluated[OMIA1206](https://omia.org/OMIA001206/9796/)
Prekallikrein deficiencyXM_019812397.2:c.2453C>TXP_019667956.2:p.(R818W)P[OMIA819](https://omia.org/OMIA000819/9796/)
Resistance to encephalomyelitisNot currently evaluated[OMIA334](https://omia.org/OMIA000334/9796/)
TwinningXM_023617086.1:c.50G>AXP_023472854.1:p.(R17K)rs3447120064Not currently evaluated[OMIA1022](https://omia.org/OMIA001022/9796/)

Guinea pig (Cavia porcellus)

DisorderGenecDNA changeProtein changersIDClassOMIA
PolydactylyNot currently evaluated[OMIA810](https://omia.org/OMIA000810/10141/)
Spermatogenic hypoplasiaXM_038583131.1:c.673T>CXP_038439059.1:p.Y225HNot currently evaluated[OMIA1136](https://omia.org/OMIA001136/10141/)
ThyroiditisXM_022419456.1:c.871C>TXP_022275164.1:p.(R291*)Not currently evaluated[OMIA1005](https://omia.org/OMIA001005/10141/)

Ferret (Mustela putorius furo)

DisorderGenecDNA changeProtein changersIDClassOMIA
Cataract, genericNot currently evaluated[OMIA168](https://omia.org/OMIA000168/9669/)

Sources

DNA-testable inherited disorders in companion animals — OMIA characterised causal variants by species, gene and pathogenicity class
Source document: OMIA — Online Mendelian Inheritance in Animals (University of Sydney)
OMIA — Online Mendelian Inheritance in Animals (University of Sydney)Nicholas, F.W., Tammen, I., & Sydney Informatics Hub. (2026). Online Mendelian Inheritance in Animals (OMIA) [dataset]. https://omia.org/. https://doi.org/10.25910/2AMR-PV70 Data made available by software support from the Sydney Informatics Hub, funded from the Ronald Bruce Anstee bequest to the Sydney School of Veterinary Science for the Anstee Hub for Inherited Diseases in Animals (AHIDA). FAIR use with attribution confirmed by OMIA curator (A/Prof I. Tammen) 2026-08-22.retrieved 2026-08-24

Verification file: pdf-raw/omia/dna_test_matrix_companion.txt